Wolff-Parkinson-White syndrome associated to scimitar syndrome. Percutaneous radiofrequency catheter ablation previous to surgical repair

Area of Science:

• Cardiology
• Electrophysiology
• Congenital Heart Disease

Background:

• Scimitar syndrome is a rare congenital anomaly characterized by anomalous pulmonary venous return.
• Wolff-Parkinson-White syndrome is a pre-excitation syndrome involving an accessory electrical pathway in the heart.
• The combined occurrence of these conditions is exceptionally rare and poses unique management challenges.

Observation:

• This case report presents the percutaneous radiofrequency ablation of a patient with Scimitar syndrome and Wolff-Parkinson-White association.
• The anatomical variants associated with Scimitar syndrome presented significant technical challenges during ablation.
• The study also includes follow-up data after surgical repair of the Scimitar syndrome.

Findings:

• Percutaneous radiofrequency ablation was successfully performed in a patient with the Scimitar syndrome-Wolff-Parkinson-White association.
• The anatomical complexities of Scimitar syndrome required tailored ablation strategies.
• Successful management involved a multidisciplinary approach combining electrophysiology and cardiothoracic surgery.

Implications:

• This case demonstrates the feasibility and safety of catheter ablation for the Wolff-Parkinson-White component in patients with Scimitar syndrome.
• It underscores the importance of experienced electrophysiologists in managing complex congenital cardiac conditions.
• Further research is warranted to establish standardized protocols for managing this rare association.